Poster Presentation 11th International Symposium on Autophagy 2025

NS1-BP as a Modulator of Stress Granule Dynamics and Autophagy in Neurodegeneration (#212)

Pureum J Jeon 1 , Hyun-Ji H Ham 1 , Haneul C Choi 1 , Semin P Park 1 , Sang-Won P Park 2 , Dong-Hyung C Cho 3 , Hyun-Jeong L Lee 4 , Hyun Kyu S Song 4 , Masaaki K Komatsu 5 , Dohyun H Han 6 , Deok-Jin J Jang 2 , Jin-A L Lee 1
  1. Departments of Biological Sciences and Biotechnology, hannam university, Daejeon, South Korea
  2. Department of Ecological Science, Kyungpook National University, sangju, Kyungpook, South Korea
  3. School of Life Sciences, BK21 FOUR KNU Creative BioRearch Group, Kyungpook National University , Daegu, Kyungpook, South Korea
  4. Department of Life Sciences, Korea University, seoul, South Korea
  5. Department of Physiology, Juntendo University Graduate School of Medicine, tokyo, Japan
  6. Department of Transdiciplinary Medicine, Seoul National University Hospital, seoul, South Korea

The NS1 binding protein, known for interacting with the influenza A virus protein, is involved in RNA processing, cancer, and nerve cell growth regulation. However, its role in stress response independent of viral infections remains unclear. This study investigates the function of NS1 binding protein in regulating stress granules during oxidative stress through interactions with GABARAP subfamily proteins. We find that NS1 binding protein localizes to stress granules, interacting with core components, GABARAP proteins, and p62, a protein involved in autophagy. In cells lacking NS1 binding protein, stress granule dynamics are altered and p62 ubiquitination is increased, suggesting impaired stress granule degradation. Overexpression of NS1 binding protein reduces p62 ubiquitination. In neurons derived from patients with amyotrophic lateral sclerosis (ALS). reduced levels of NS1 binding protein and p62 disrupt stress granule morphology. Recently, we performed LC-MS/MS-based proteomic analysis to identify NS1 binding protein-interacting partners and discovered additional candidates involved in stress granule dynamics and autophagy regulation. These findings identify NS1 binding protein as a negative regulator of p62 ubiquitination and a facilitator of GABARAP recruitment to stress granules, implicating it in stress granule regulation and the pathogenesis of ALS.